Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.
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Barium enema showing megarectum. Anorectal manometry shows lack of relaxation of internal anal sphincter in response to rectal distension.
Vólvulo en adultos
Peritoneal irritation was not found. The girl was discharged on the 5th day after surgery.
Abdominal X-rays showed a dilated colon occupying abdominal cavity. Enfermedad de Hirschsprung en un adulto. The analytical study was normal.
Enfermedad de Hirschprung del adulto
This segment is everted and extracted by transanal enfermevad. These radiological images were consistent with Hirschsprung’s disease; for this reason, we extracted surgically the fecal mass through the anus. Hirschsprung’s disease; Congenital megacolon; Fecal incontinence. Hirschsprung’s disease in a young adult: In this latter case, HD may affect the entire colon and even the small intestine. Imaging studies such as computed tomography CT and barium enemas are usually accepted for evaluation of chronic constipation, which is a common disorder in adults.
Physical examination revealed a mildly distended abdomen and no other relevant enfermedzd. A year-old man came to the emergency room because of diarrhea of 4 weeks duration, accompanied by constipation.
The clinical presentation changes between children and adults. HD occurs in approximately 1 in live hirchsprung. Hospital Universitario Virgen Macarena.
No abnormalities resulted from the rectal examination. A year-old male was admitted in the Emergency Department by generalized abdominal pain accompanied by anorexia of several days duration. The rectal biopsy should be made on the back side of rectum, about 6 cm height, and it shows absence of ganglion cells, nerve fibers hyperplasia and an increased level of acetylcholinesterase 7.
Another option in these cases is the realization of an end ileostomy following colectomy, to avoid the risk of a possible wound dehiscence, as it happened in our case. Observing the Meissner and Auerbach plexus with immunohistochemical techniques and enolase S, loss of neurons ganglion cells and lower density of such plexuses were observed with respect to a normal colon Figs.
Some authors have maintained that Hirschsprung’s disease in adults probably correspond to congenital cases not diagnosed previously, and consequently it is likely that, in fact, adult Enfermecad disease does not really exist as an independent entity.
Wall of the rectum re aganglionosis consistent with Hirschsprung’s disease fig.
English pdf Spanish pdf Article in xml format Article references How to cite this article Automatic translation Send this article by e-mail. Enfermedad de Hirschsprung en adultos. The authors declare that there is no conflict of interest. J Forensic Sci ; IHC x positive for S in the nerve plexuses. The scientific works include the areas of Clinical, Endoscopic, Surgical, and Pediatric Gastroenterology, along with related disciplines. S protein detection of neuronal cells: Discussion Hirschsprung’s disease affects about 1 in 5, live births and usually presents in neonatal period.
Based on the length of the affected segment, it is classified as: The infrequency of this diagnosis in this age and the clinical hirschspdung of this patient underscore afultos uniqueness of this ihrschsprung. The patient was a 32 year old man with severe intellectual and mental retardation from a poorly educated family.
The patient was discharged in good general health and tolerating normal food. In this case, the aganglionic segment hirschspryng not removed, but a rear dissection is performed.
It usually presents as severe constipation with colonic dilatation proximal to the aganglionic segment. The diagnosis is made by barium enema, anorectal manometry and rectal biopsy.
Peripheral aerial imagery was found in the dilated segment, gas-like wall, which is thickened in this segment.
Introduction Hirschsprung’s Disease HDalso known as congenital aganglionic megacolon, is an anomaly characterized by an absence of ganglion cells in the myenteric and submucosal plexuses in a variable bowel segment. Treatment is always surgical.
Rev Esp Enferm Dig, 3pp. Enfermedad de Hirschsprung del adulto: Only cases of HD have been described in adults, with male predominance in a 4: Adultoos had worsened in recent months, prompting her to seek the evaluation of a proctologist.
The treatment is surgical, removing the aganglionic segment and restoring continuity of digestive tract. The diagnosis of HD is supported by barium enema studies, anorectal manometry and rectal biopsy. Standing and prone abdominal radiography showed x-ray opacity compatible with fecal matter.